Yasui procedure results: A multicenter retrospective study


Soynov I.A. Gorbatykh A.V. Amansakhatova E.N. Arkhipov A.N. Avramenko A.A. Gorbunov D.V. Grekhov E.V. Kazantsev K.B. Kolbik V.G. Kulyabin Y.Y. Linnik Y.I. Manukian S.N. Movsesyan R.R. Nichay N.R. Petrushenko D.Y. Plotnikov M.V. Teplov P.V. Kornilov I.A. Drozdovski K.
December 2025Elsevier Ireland Ltd

Progress in Pediatric Cardiology
2025#79

Background: Aortic atresia or stenosis with ventricular septal defect (VSD) is a rare congenital heart defect. In 1987, Yasui introduced a biventricular repair for severe subaortic obstruction and subaortic VSD. Contemporary series report early mortality <15 %. Comparative inferences by surgical strategy remain limited by small samples, with the largest published series including 25 patients. Objectives: To evaluate the outcomes and complications following primary versus staged Yasui procedures. Methods: Retrospective multicenter study included 26 patients who underwent the Yasui procedure at 10 cardiac surgery centers in Russia, Belarus, and Kazakhstan (2008–2023). Results: There were no deaths in the primary Yasui group; 12-month survival in the staged Yasui group was 76.9 % (95 % CI: 54 %–88 %, p = 0.08). Freedom from reoperation at 92 months was 58.9 % (95 % CI: 23.5 %–82.4 %) in the primary Yasui group and 34.0 % (95 % CI: 9.1 %–61.6 %) in the staged group. Freedom from left ventricular outflow tract obstruction (LVOT) at 60 months was 76 % (95 % CI: 30.7 %–93.9 %) in the primary Yasui group and 57 % (95 % CI: 21.7 %–81.5 %) in the staged Yasui group. Conclusions: In this multicenter descriptive series, biventricular repair using the Yasui procedure was feasible and associated with low early mortality in selected patients with hypoplastic left heart syndrome (HLHS) and associated VSD. Within the limits of this small retrospective cohort, surgical strategy (primary vs staged Yasui) did not appear to affect mortality, reoperation, or the incidence of LVOT obstruction.

Aortic atresia , Aortic stenosis , Congenital heart defects , Yasui procedure

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Federal State Budgetary Institution, Meshalkin National Medical Research Center, Ministry of Health of the Russian Federation, Novosibirsk, Russian Federation
Federal State Budgetary Institution, Almazov National Medical Research Center, Ministry of Health of the Russian Federation, Saint-Petersburg, Russian Federation
Novosibirsk State University, Russian Federation
Federal State Budgetary Educational Institution of Higher Education, Samara State Medical University, Ministry of Healthcare of the Russian Federation, Russian Federation
Samara Regional Clinical Cardiac Hospital named after V.P. Polyakov, Russian Federation
National Research Cardiac Surgery Center, Astana, Kazakhstan
Sverdlovsk Regional Clinical Hospital No. 1, Ministry of Health of the Russian Federation, Russian Federation
State Institution “Republican Scientific and Practical Center of Pediatric Surgery”, Minsk, Belarus
Childrens City Multidisciplinary Clinical Specialized Center for High Medical Technologies, Saint-Petersburg, Russian Federation
Mechnikov North-Western State Medical University, Russian Federation
Cardiovascular Department, Novosibirsk State Medical University, Ministry of Health of Russian Federation, Russian Federation
State Autonomous Healthcare Institution, Childrens Republican Clinical Hospital of the Ministry of Health of the Republic of Tatarstan, Russian Federation
Federal Center for Cardiovascular Surgery, Ministry of Health of the Russian Federation, Astrakhan, Russian Federation
Federal Center for Cardiovascular Surgery, Ministry of Health of the Russian Federation, Krasnoyarsk, Russian Federation
Milton S. Hershey Medical Center, Penn State University College of Medicine, Hershey, PA, United States

Federal State Budgetary Institution
Federal State Budgetary Institution
Novosibirsk State University
Federal State Budgetary Educational Institution of Higher Education
Samara Regional Clinical Cardiac Hospital named after V.P. Polyakov
National Research Cardiac Surgery Center
Sverdlovsk Regional Clinical Hospital No. 1
State Institution “Republican Scientific and Practical Center of Pediatric Surgery”
Childrens City Multidisciplinary Clinical Specialized Center for High Medical Technologies
Mechnikov North-Western State Medical University
Cardiovascular Department
State Autonomous Healthcare Institution
Federal Center for Cardiovascular Surgery
Federal Center for Cardiovascular Surgery
Milton S. Hershey Medical Center

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